Studienliteratur zu Immunologischen Erkrankungen
Zuletzt geändert: 24.06.2026 https://kinderkrebsinfo.de/doi/e123842
Studienliteratur Hämophagozytische Lymphohistiozytose (HLH) 
- Zivkovic K, Bergsten E, Aricó M, Astigarraga I, Ishii E, Ladisch S, Lehmberg K, Minkov M, Nanduri V, Henter JI: Assessment of intrathecal therapy in the treatment of familial haemophagocytic lymphohistiocytosis. British journal of haematology 2026, 208: 705 [PMID: 41243379]
- Hägele P, Staus P, Scheible R, Uhlmann A, Heeg M, Klemann C, Maccari ME, Ritterbusch H, Armstrong M, Cutcutache I, Elliott KS, von Bernuth H, Leahy TR, Leyh J, Holzinger D, Lehmberg K, Svec P, Masjosthusmann K, Hambleton S, Jakob M, Sparber-Sauer M, Kager L, Puzik A, Wolkewitz M, Lorenz MR, Schwarz K, Speckmann C, Rensing-Ehl A, Ehl S, ALPID study group: Diagnostic evaluation of paediatric autoimmune lymphoproliferative immunodeficiencies (ALPID): a prospective cohort study. The Lancet. Haematology 2024, 11:e114-e126 [PMID: 38302222]
- Böhm S, Wustrau K, Pachlopnik Schmid J, Prader S, Ahlmann M, Yacobovich J, Beier R, Speckmann C, Behnisch W, Ifversen M, Jordan M, Marsh R, Naumann-Bartsch N, Mauz-Körholz C, Hönig M, Schulz A, Malinowska I, Hines M, Nichols KE, Gil-Herrera J, Talano JA, Crooks B, Formankova R, Jorch N, Bakhtiar S, Kühnle I, Streiter M, Nathrath M, Russo A, Dürken M, Lang P, Lindemans C, Henter JI, Lehmberg K, Ehl S: Survival in primary hemophagocytic lymphohistiocytosis, 2016 to 2021: etoposide is better than its reputation. Blood 2024, 143: 872 [PMID: 37992218]
- Zoref-Lorenz A, Lehmberg K, Jordan M: Hemophagocytic Lymphohistiocytosis in the Context of Hematological Malignancies and Solid Tumors. Advances in experimental medicine and biology 2024, 1448, 429 [PMID: 39117831]
- Dettmer-Monaco V, Weißert K, Ammann S, Monaco G, Lei L, Gräßel L, Rhiel M, Rositzka J, Kaufmann MM, Geiger K, Andrieux G, Lao J, Thoulass G, Schell C, Boerries M, Illert AL, Cornu TI, Ehl S, Aichele P, Cathomen T: Gene editing of hematopoietic stem cells restores T-cell response in familial hemophagocytic lymphohistiocytosis. The Journal of allergy and clinical immunology 2023, [PMID: 37595758]
- Toskov V, Ehl S: Autoimmune lymphoproliferative immunodeficiencies (ALPID) in childhood: breakdown of immune homeostasis and immune dysregulation. Molecular and cellular pediatrics 2023, 10: 11 [PMID: 37702894]
- Magerus A, Rensing-Ehl A, Rao VK, Teachey D, Rieux-Laucat F, Ehl S: Autoimmune-lymphoproliferative immunodeficiencies (ALPID) A proposed approach to redefining ALPS and other lymphoproliferative immune disorders. The Journal of allergy and clinical immunology 2023 Nov 15; [PMID: 37977527]
- Böhm S, Wustrau K, Pachlopnik Schmid J, Prader S, Ahlman M, Yacobovich J, Beier R, Speckmann C, Behnisch W, Ifversen M, Jordan MB, Marsh RA, Naumann-Bartsch N, Mauz-Koerholz C, Honig M, Schulz AS, Malinowska I, Hines MR, Nichols KE, Gil-Herrera J, Talano JA, Crooks B, Formankova R, Jorch N, Bakhtiar S, Kühnle I, Streiter M, Nathrath M, Russo A, Duerken M, Lang P, Lindemans CA, Henter JI, Lehmberg K, Ehl S: Survival in primary hemophagocytic lymphohistiocytosis 2016-2021: etoposide is better than its reputation. Blood 2023 Nov 22; [PMID: 37992218]
- Hines MR, von Bahr Greenwood T, Beutel G, Beutel K, Hays JA, Horne A, Janka G, Jordan MB, van Laar JAM, Lachmann G, Lehmberg K, Machowicz R, Miettunen P, La Rosée P, Shakoory B, Zinter MS, Henter JI: Consensus-Based Guidelines for the Recognition, Diagnosis, and Management of Hemophagocytic Lymphohistiocytosis in Critically Ill Children and Adults. Critical care medicine 2022, 50: 860 [PMID: 34605776]
- Ehl S, von Bahr Greenwood T, Bergsten E, Fischer A, Henter JI, Hines M, Lehmberg K, Janka G, Moshous D, Nichols KE: Is neutralization of IFN-γ sufficient to control inflammation in HLH? Pediatric blood & cancer 2021, 68:e28886 [PMID: 33405364]
- Wegehaupt O, Wustrau K, Lehmberg K, Ehl S: Cell Versus Cytokine - Directed Therapies for Hemophagocytic Lymphohistiocytosis (HLH) in Inborn Errors of Immunity. Frontiers in immunology 2020, 11: 808 [PMID: 32457750]
- Ehl S, Astigarraga I, von Bahr Greenwood T, Hines M, Horne A, Ishii E, Janka G, Jordan MB, La Rosée P, Lehmberg K, Machowicz R, Nichols KE, Sieni E, Wang Z, Henter JI: Recommendations for the Use of Etoposide-Based Therapy and Bone Marrow Transplantation for the Treatment of HLH: Consensus Statements by the HLH Steering Committee of the Histiocyte Society. The journal of allergy and clinical immunology. In practice 2018, 6: 1508 [PMID: 30201097]
- Ehl S, Bogdan C, Niehues T, Borchard G, Baumann U, Hecht J, Koch j, Neubert J, Wiese-Pochelt K, Zepp F: Impfen bei Immundefizienz : Anwendungshinweise zu den von der Ständigen Impfkommission empfohlenen Impfungen.(II) Impfen bei 1. Primären Immundefekterkrankungen und 2. HIV-Infektion. Bundesgesundheitsblatt 2018, 61: 1034 [PMID: 30062550]
- Lehmberg K, Ehl S: Hämophagozytische Lymphohistiozytose. Pädiatrische Hämatologie und Onkologie, Hrsg: A. Eggert, C. Niemeyer, Springer Verlag 2. Auflage 2018 [ISSN: 978-3-662-43686-8]
- Ehl S: Etoposide for HLH: the limits of efficacy. Blood 2017, 130: 2692 [PMID: 29269529]
- Lehmberg K, Nichols KE, Henter JI, Girschikofsky M, Greenwood T, Jordan M, Kumar A, Minkov M, La Rosée P, Weitzman S: Consensus recommendations for the diagnosis and management of hemophagocytic lymphohistiocytosis associated with malignancies. Haematologica 2015, 100: 997 [PMID: 26314082]
- Lehmberg K, Sprekels B, Nichols KE, Woessmann W, Müller I, Suttorp M, Bernig T, Beutel K, Bode SF, Kentouche K, Kolb R, Längler A, Minkov M, Schilling FH, Schmid I, Vieth S, Ehl S, Zur Stadt U, Janka GE: Malignancy-associated haemophagocytic lymphohistiocytosis in children and adolescents. Br J Haematol 2015, 170: 539 [PMID: 25940575]
- Trottestam H, Berglöf E, Horne A, Onelöv E, Beutel K, Lehmberg K, Sieni E, Silfverberg T, Aricò M, Janka G, Henter JI: Risk factors for early death in children with haemophagocytic lymphohistiocytosis. Acta paediatrica (Oslo, Norway : 1992) 2012, 101: 313 [PMID: 22017632]
- Pagel J, Beutel K, Lehmberg K, Koch F, Maul-Pavicic A, Rohlfs AK, Al-Jefri A, Beier R, Bomme Ousager L, Ehlert K, Gross-Wieltsch U, Jorch N, Kremens B, Pekrun A, Sparber-Sauer M, Mejstrikova E, Wawer A, Ehl S, zur Stadt U, Janka G: Distinct mutations in STXBP2 are associated with variable clinical presentations in patients with familial hemophagocytic lymphohistiocytosis type 5 (FHL5). Blood 2012, 119: 6016 [PMID: 22451424]
- Janka GE: Familial and acquired hemophagocytic lymphohistiocytosis. Annual review of medicine 2012, 63: 233 [PMID: 22248322]
- Trottestam H, Horne A, Aricò M, Egeler RM, Filipovich AH, Gadner H, Imashuku S, Ladisch S, Webb D, Janka G, Henter JI, Histiocyte Society: Chemoimmunotherapy for hemophagocytic lymphohistiocytosis: long-term results of the HLH-94 treatment protocol. Blood 2011, 118: 4577 [PMID: 21900192]
- Janka GE: Hemophagocytic syndromes. Blood reviews 2007, 21: 245 [PMID: 17590250]
- Henter JI, Horne A, Aricó M, Egeler RM, Filipovich AH, Imashuku S, Ladisch S, McClain K, Webb D, Winiarski J, Janka G: HLH-2004: Diagnostic and therapeutic guidelines for hemophagocytic lymphohistiocytosis. Pediatric blood & cancer 2007, 48: 124 [PMID: 16937360]
- Ouachée-Chardin M, Elie C, de Saint Basile G, Le Deist F, Mahlaoui N, Picard C, Neven B, Casanova JL, Tardieu M, Cavazzana-Calvo M, Blanche S, Fischer A: Hematopoietic stem cell transplantation in hemophagocytic lymphohistiocytosis: a single-center report of 48 patients. Pediatrics 2006, 117:e743 [PMID: 16549504]
- Filipovich AH: Life-threatening hemophagocytic syndromes: current outcomes with hematopoietic stem cell transplantation. Pediatric transplantation 2005, 9 Suppl 7: 87 [PMID: 16305623]
- Imashuku S, Kuriyama K, Sakai R, Nakao Y, Masuda S, Yasuda N, Kawano F, Yakushijin K, Miyagawa A, Nakao T, Teramura T, Tabata Y, Morimoto A, Hibi S: Treatment of Epstein-Barr virus-associated hemophagocytic lymphohistiocytosis (EBV-HLH) in young adults: a report from the HLH study center. Medical and pediatric oncology 2003, 41: 103 [PMID: 12825212]
- Henter JI, Samuelsson-Horne A, Aricò M, Egeler RM, Elinder G, Filipovich AH, Gadner H, Imashuku S, Komp D, Ladisch S, Webb D, Janka G, Histocyte Society: Treatment of hemophagocytic lymphohistiocytosis with HLH-94 immunochemotherapy and bone marrow transplantation. Blood 2002, 100: 2367 [PMID: 12239144]
- Holter W, Ressmann G, Grois N, Lehner M, Parolini O, Gadner H: Normal monocyte-derived dendritic cell function in patients with Langerhans-cell-histiocytosis. Medical and pediatric oncology 2002, 39: 181 [PMID: 12210447]
- Imashuku S: Clinical features and treatment strategies of Epstein-Barr virus-associated hemophagocytic lymphohistiocytosis. Critical reviews in oncology/hematology 2002, 44: 259 [PMID: 12467966]
- Imashuku S, Kuriyama K, Teramura T, Ishii E, Kinugawa N, Kato M, Sako M, Hibi S: Requirement for etoposide in the treatment of Epstein-Barr virus-associated hemophagocytic lymphohistiocytosis. Journal of clinical oncology : official journal of the American Society of Clinical Oncology 2001, 19: 2665 [PMID: 11352958]
- Dürken M, Finckenstein FG, Janka GE: Bone marrow transplantation in hemophagocytic lymphohistiocytosis. Leukemia & lymphoma 2001, 41(1-2): 89 [PMID: 11342360]
- Baker KS, DeLaat CA, Steinbuch M, Gross TG, Shapiro RS, Loechelt B, Harris R, Filipovich AH: Successful correction of hemophagocytic lymphohistiocytosis with related or unrelated bone marrow transplantation. Blood 1997, 89: 3857 [PMID: 9160694]
- Henter J, Arico M, Egeler R, Elinder G, Favara B, Filipovich A, Gadner H, Imashuku S, Janka-Schaub G, Komp D, Ladisch S, Webb D: HLH-94: a treatment protocol for hemophagocytic lymphohistiocytosis. HLH study Group of the Histiocyte Society. Med Pediatr Oncol 1997, 28: 342 [PMID: 9121398]
- Henter JI, Elinder G, Ost A: Diagnostic guidelines for hemophagocytic lymphohistiocytosis. The FHL Study Group of the Histiocyte Society. Seminars in oncology 1991, 18: 29 [PMID: 1992521]
- Blanche S, Caniglia M, Girault D, Landman J, Griscelli C, Fischer A: Treatment of hemophagocytic lymphohistiocytosis with chemotherapy and bone marrow transplantation: a single-center study of 22 cases. Blood 1991, 78: 51 [PMID: 2070059]
